Cardiac surgical aspects of Down syndrome
نویسندگان
چکیده
Results 82,5% (n = 28) had hard combined CHD, 82,4% (n = 28) high pulmonary hypertension, all patients heart failure. In 20,6% (n = 6) patients heart catheterization was performed. 6 (20,6%) kids received only medical treatment: 2 (5,8%) inoperable, 3 (8,8%) medical preparation for surgery due to PH, 1 (2,9%) no need of surgery. 28 (82,4%) patients were operated on. 26 (92,8%) were open heart cases. 57,6% (n = 15) underwent septal defects (ASD, VSD) plasty at median age of 12 ± 3 months. In 42,3% (n = 11) AVSD was corrected at median age of 6 ± 1 month. In 7 patients (23,6%) postoperative period was complicated by: DIC syndrome (57,1%), sepsis (28,6%), chylothorax (14,3%). 30-day in hospital mortality occurred in 3 (10,7%) cases: 1 (14,3%) – due to intractable pulmonary hypertensive crisis; 1 (14,3%) – sepsis; 1 (14,3%) – sepsis associated with DIC syndrome. Neither late death nor any residual defects requiring reoperation were detected at follow up.
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